Case Report
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A Case With Rapidly Progressive Cardiac Fibroma

Year 2016, Volume: 30 Issue: 1, 35 - 38, 24.06.2016

Abstract

Cardiac tumours are rarely seen in childhood. Approximately 90% of these
tumors are benign and the most common benign tumor is rhabdomyoma. Fibroma,
teratoma and mixoma are the other causes of benign cardiac masses. In this case
we presented a newborn in whom a cardiac mass was detected in echocardiographic
examination. This cardiac mass grew significantly during the postnatal 7
months. Due to rapid progression and left ventricular outflow obstruction, the
mass was excised. Histopathological examination confirmed the diagnosis of
fibroma. Briefly, giant masses which cause permanent rhythm abnormalities,
myocardial dysfunction and ventricular inflow or outflow obstruction should be
removed surgically.


References

  • Referans1 Gerald RM, Adrian MM. Cardiac Tumors. İn:Allen HD, Driscoll DJ, Shaddy RE, Feltes T eds. Moss and Adams' Heart disease in Infants, Children, and Adolescents: Including the Fetus and Young Adult. 8.ed. Philadelphia: Lippincott Williams & Wilkins; 2013 Chapter 72.p.1549-1564.
  • Referans2 Uzun O, Wilson DG, Vujanic GM, Parsons JM, Giovanni J . Cardiac tumours in children. Orphanet Journal of Rare Diseases. 2007;2:11.
  • Referans3 Padolino MA, Vida VL, Boccuzzo G, Tonello M, Sarris GE, Berggren H et al. Surgery for Primary Cardiac Tumors in Children Early and Late Results in a Multicenter European Congenital Heart Surgeons Association Study Circulation. 2012;126:22-30.
  • Referans4 Yadava OP. Cardiac tumours in infancy. Indian Heart Journal. 2012;64:492-496.
  • Referans5 Kır M, Çatalyürek H, Karadaş U, Ünal N, Saylam G. A prenatally diagnosed newborn with an intracardiac rhabdomyoma obstructing the left ventricular outflow tract. Türk Göğüs Kalp Damar Cerrahisi Dergisi 2011;19(4):623-626.
  • Referans6 Kobayashi D, L’Ecuyer T, Aggarwal S. Orthotopic Heart Transplant: A Therapeutic Option for Unresectable Cardiac Fibroma in Infants. Congenit Heart Dis. 2012;7:31–36.

Progresif Seyreden Kardiyak Fibromalı Bir Olgu

Year 2016, Volume: 30 Issue: 1, 35 - 38, 24.06.2016

Abstract

Çocukluk döneminde kalp tümörleri oldukça nadir
görülür. Bu tümörlerin yaklaşık %90'ı iyi huyludur ve en sık görülen primer iyi
huylu tümörler rabdomiyomlardır. Fibroma, miksoma ve teratama ise daha nadir
görülen primer iyi huylu tümörlerdir. Bu yazıda yenidoğan döneminde yapılan
ekokardiyografisinde kardiyak kitle saptanan bir olgu sunuldu. Kardiyak kitle 7
aylık izlem süresince belirgin olarak büyüdü. Hızlı ilerleme göstermesi ve sol
ventrikül çıkım yoluna doğru uzanması nedeni kitle total olarak çıkartıldı. Dev
kardiyak kitleye cerrahi sonrası fibroma tanısı konuldu. Kardiyak kitleler
ventrikül giriş ve çıkış yolu darlığı, ritim bozukluğu ve hemodinamik bozukluk
oluşturduğu zaman çıkartılmaları gerekmektedir.




References

  • Referans1 Gerald RM, Adrian MM. Cardiac Tumors. İn:Allen HD, Driscoll DJ, Shaddy RE, Feltes T eds. Moss and Adams' Heart disease in Infants, Children, and Adolescents: Including the Fetus and Young Adult. 8.ed. Philadelphia: Lippincott Williams & Wilkins; 2013 Chapter 72.p.1549-1564.
  • Referans2 Uzun O, Wilson DG, Vujanic GM, Parsons JM, Giovanni J . Cardiac tumours in children. Orphanet Journal of Rare Diseases. 2007;2:11.
  • Referans3 Padolino MA, Vida VL, Boccuzzo G, Tonello M, Sarris GE, Berggren H et al. Surgery for Primary Cardiac Tumors in Children Early and Late Results in a Multicenter European Congenital Heart Surgeons Association Study Circulation. 2012;126:22-30.
  • Referans4 Yadava OP. Cardiac tumours in infancy. Indian Heart Journal. 2012;64:492-496.
  • Referans5 Kır M, Çatalyürek H, Karadaş U, Ünal N, Saylam G. A prenatally diagnosed newborn with an intracardiac rhabdomyoma obstructing the left ventricular outflow tract. Türk Göğüs Kalp Damar Cerrahisi Dergisi 2011;19(4):623-626.
  • Referans6 Kobayashi D, L’Ecuyer T, Aggarwal S. Orthotopic Heart Transplant: A Therapeutic Option for Unresectable Cardiac Fibroma in Infants. Congenit Heart Dis. 2012;7:31–36.
There are 6 citations in total.

Details

Journal Section Articles
Authors

Tülay Demircan

Özgür Kızılca This is me

Mustafa Kır This is me

Baran Uğurlu This is me

Nurettin Ünal This is me

Publication Date June 24, 2016
Submission Date December 22, 2014
Published in Issue Year 2016 Volume: 30 Issue: 1

Cite

Vancouver Demircan T, Kızılca Ö, Kır M, Uğurlu B, Ünal N. Progresif Seyreden Kardiyak Fibromalı Bir Olgu. J DEU Med. 2016;30(1):35-8.