PEUTZ - JEGHERS SENDROMU VE JEJUNAL İNTUSSUSSEPSİYON: BİR OLGUNUN SUNUMU

Özer Makay; M. Gökhan Ünsal; Erhan Akgün; Halit Osmanoğlu

EN TR

PEUTZ-JEGHERS SYNDROME AND JEJUNAL INTUSSUSEPTION : A CASE REPORT

Abstract

Peutz-Jeghers syndrome is an autosomal dominant inherited disorder characterized by gastrointestinal hamartomatous polyps in association with mucocutaneous melanocytic pigmentation. Although this syndrome is rare, patient follow-up care should be done a life long since the increased risk for intussusception secondary to bowel obstruction and malignancy in the elderly. This case report presents a 33-year-old male with Peutz-Jeghers syndrome diagnosed at the age of 18. The patient admitted with symptoms like abdominal pain, nausea and vomitting, especially increasing postprandial. Enteroclysis study revealed 2 polyps located in the jejenum, each 4 cm in diameter, and a jejuno-jejunal intussusception, originating from these polips. A laparomy was carried out and the intussusception was restored manually. Enterotomy was performed to treat polyps by polypectomy. It is suggested that patients with Peutz-Jeghers syndrome should also be monitored for intestinal intussusception and bowel ischemia. Early diagnosis is fundamental.

Keywords

peutz-Jeghers syndrome, intussusception, polypectomy

Details

Primary Language

Turkish

Subjects

-

Journal Section

-

Authors

Özer Makay

M. Gökhan Ünsal

Erhan Akgün

Halit Osmanoğlu

Publication Date

June 1, 2005

Submission Date

June 1, 2005

Acceptance Date

-

Published in Issue

Year 2005 Volume: 44 Number: 2

IZ

https://izlik.org/JA93PY95RL

Cite

RIS / Bibtex

Vancouver

1.Özer Makay, M. Gökhan Ünsal, Erhan Akgün, Halit Osmanoğlu. PEUTZ - JEGHERS SENDROMU VE JEJUNAL İNTUSSUSSEPSİYON: BİR OLGUNUN SUNUMU. EJM [Internet]. 2005 Jun. 1;44(2):131-3. Available from: https://izlik.org/JA93PY95RL

PEUTZ-JEGHERS SYNDROME AND JEJUNAL INTUSSUSEPTION : A CASE REPORT

Abstract

Keywords