Fulminan hepatik yetmezlikle başvuran hemofagositik sendromlu bir olgu

Gülen H; Aslan Ş; Şimşek A; Ayhan S; Moumin N; Kasırga E

EN TR

A case of hemophagocytic syndrome that presented as fulminant hepatic failure

Abstract

Hemophagocytic lymphohistiocytosis (HLH) is an uncommon clinical entity characterized by fever, pancytopenia, hepatosplenomegaly and hemophagocytosis in bone marrow, liver or lymph nodes. Fulminant hepatic failure (FHF) is a clinical syndrome resulting from massive necrosis of hepatocytes or severe functional impairment of hepatocytes in a patient who does not have a pre-existing liver disease. Hepatic manifestations are common in hemophagocytic lymphohistiocytosis and overt hepatic failure may occur, but initial presentation as fulminant hepatic failure is not well recognized. We report the case of a 9 year old girl presented with fulminant hepatic failure and “Hemophagocytic lymphohistiocytosis” should be considered in the differential diagnosis of fulminant hepatic failure in children.

Keywords

Hemophagocytic lymphohistiocytosis; fulminant hepatic failure, child

Details

Primary Language

Turkish

Subjects

-

Journal Section

-

Authors

Gülen H

Aslan Ş

Şimşek A

Ayhan S

Moumin N

Kasırga E

Publication Date

September 1, 2011

Submission Date

September 1, 2011

Acceptance Date

-

Published in Issue

Year 1970 Volume: 50 Number: 3

IZ

https://izlik.org/JA64YB97UK

Cite

RIS / Bibtex

Vancouver

1.Gülen H, Aslan Ş, Şimşek A, Ayhan S, Moumin N, Kasırga E. Fulminan hepatik yetmezlikle başvuran hemofagositik sendromlu bir olgu. EJM [Internet]. 2011 Sep. 1;50(3):193-6. Available from: https://izlik.org/JA64YB97UK

A case of hemophagocytic syndrome that presented as fulminant hepatic failure

A case of hemophagocytic syndrome that presented as fulminant hepatic failure

Abstract

Keywords