Psödoksantoma elastikum ve kalsinozis kutis

Pala E; Bayol Ü; Usturalı Keskin E; Küçük Ü; Türe G Bıçakçı C

EN TR

Pseudoxanthoma elasticum and calcinosis cutis

Abstract

Pseudoxanthoma elasticum (PXE) is an inherited multisystem disorder with ectopic mineralization of connective tissues and characteristic clinical manifestations in the skin, eyes and cardiovascular system. A 46-year-old woman was admitted to dermatology clinic with whitish/yellow papules that coalesce into cobblestone patterned plaques at the lateral, posterior aspect of the neck 6 previously. Two of the lesions were excised by plastic surgery. Histologically fragmented calcified elastic fibers were seen in the affected elastic tissue of the dermis accompanied by dystrophic calcinosis cutis in the superficial dermis. Fundoscopic examination revealed bilateral angioid streaks and peau d'orange lesions. Because of the typical skin findings proved by biopsy and ocular involvement, our diagnosis was PXE. We should be aware of this entity since PXE is associated with considerable morbidity and mortality. The second important point is when we note calcinosis cutis, we should look for elastic tissue damage since calcium prefers depositing in those areas.

Keywords

Pseudoxanthoma elasticum, calcinosis

Details

Primary Language

Turkish

Subjects

-

Journal Section

-

Authors

Pala E

Bayol Ü

Usturalı Keskin E

Küçük Ü

Türe G Bıçakçı C

Publication Date

December 1, 2013

Submission Date

December 1, 2013

Acceptance Date

-

Published in Issue

Year 1970 Volume: 52 Number: 4

IZ

https://izlik.org/JA76MN82TK

Cite

RIS / Bibtex

Vancouver

1.Pala E, Bayol Ü, Usturalı Keskin E, Küçük Ü, Türe G Bıçakçı C. Psödoksantoma elastikum ve kalsinozis kutis. EJM [Internet]. 2013 Dec. 1;52(4):214-6. Available from: https://izlik.org/JA76MN82TK

Pseudoxanthoma elasticum and calcinosis cutis

Pseudoxanthoma elasticum and calcinosis cutis

Abstract

Keywords