Kalp ve beyin tutulumlu Erdheim-Chester hastalığı

Yasemin Çiğdem Özerdem; Bahar Müezzinoğlu; Gür Akansel; Muhip Kanko; Hüsnü Efendi

doi:10.19161/etd.344134

EN TR

Cardiac and cerebral involvement in Erdheim-Chester disease

Abstract

Erdheim-Chester disease (ECD) is a rare non-Langerhans form of systemic histiocytosis of unknown etiology that progresses with multiple organ involvement. It is characterized by a xanthomatous infiltration showing positive staining with CD68 and negative staining with CD1a in tissues. We report a 62 year-old case complaining of malodor, in the brain magnetic resonance imaging of whom a mass was found at the clivus and leptomeningeal involvement was determined. The accompanying intracardiac mass was excised and the case was diagnosed histopathologically as ECD. We present the unusual clinical symptoms along with histopathologic and radiodiagnostic findings and discuss the differential diagnosis of this rare disease.

Keywords

Erdheim-Chester disease, magnetic resonance imaging, cardiac involvement, neurological signs

Details

Primary Language

Turkish

Subjects

-

Journal Section

-

Authors

Yasemin Çiğdem Özerdem

Bahar Müezzinoğlu

Gür Akansel

Muhip Kanko

Hüsnü Efendi

Publication Date

September 1, 2015

Submission Date

September 1, 2015

Acceptance Date

-

Published in Issue

Year 2015 Volume: 54 Number: 3

DOI

https://doi.org/10.19161/etd.344134

IZ

https://izlik.org/JA33RT28SW

Cite

RIS / Bibtex

Vancouver

1.Yasemin Çiğdem Özerdem, Bahar Müezzinoğlu, Gür Akansel, Muhip Kanko, Hüsnü Efendi. Kalp ve beyin tutulumlu Erdheim-Chester hastalığı. EJM. 2015 Sep. 1;54(3):134-6. doi:10.19161/etd.344134

Cardiac and cerebral involvement in Erdheim-Chester disease

Abstract

Keywords