Beta -2 mikroglobulin amiloidozu (Aβ2M) (diyalizle ilişkili amiloidoz)

Cilt: 48 Sayı: 2 1 Haziran 2009
  • Sarsık B
  • Doğanavşargil B
  • Bozkurt D
  • Şen S
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Beta-2 microglobulin amyloidosis (Aβ2M) (dialysis related amyloidosis)

Abstract

Dialysis-related amyloidosis secondary to β2 microglobulin deposition is a complication of long-term dialysis. Beta2 microglobulin has a tendency to deposit in the osteoarticular tissues, particularly in large bones and in synovial membranes. Clinical manifestations include carpal tunnel syndrome, destructive arthropathy, bone cysts and fractures. We diagnosed a patient with β2 microglobulin amyloidosis in whom cystic lesion and destructive arthropathy were clinically showed. The patient was a 53-year-old man who had been on hemodialysis for more than 15 years because of end-stage renal disease. Congo red staining and β2 microglobulin immunohistochemistry, showed extended β2 microglobulin deposits in the operation material was taken because of the pathological fracture of femur .

Keywords

Ayrıntılar

Birincil Dil

Türkçe

Konular

-

Bölüm

-

Yazarlar

Sarsık B

Doğanavşargil B

Bozkurt D

Şen S

Yayımlanma Tarihi

1 Haziran 2009

Gönderilme Tarihi

1 Haziran 2009

Kabul Tarihi

-

Yayımlandığı Sayı

Yıl 1970 Cilt: 48 Sayı: 2

Kaynak Göster

Vancouver
1.Sarsık B, Doğanavşargil B, Bozkurt D, Şen S. Beta -2 mikroglobulin amiloidozu (Aβ2M) (diyalizle ilişkili amiloidoz). ETD [Internet]. 01 Haziran 2009;48(2):139-43. Erişim adresi: https://izlik.org/JA88WW45LZ

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